Bophelo, Mafu a le Maemo
Lou Gehrig ya lefu. Mokhoa oa ho sebetsana le lefu lena Charcot?
Charcot e lefu - se e le mokhoa oa ho bontša? Hore re nehela hlahiswa ka sehlooho sena.
Tlhaloso ya lefu lena
Charcot Syndrome (kapa hill claudication) ke lefu le tšoauoa ka ponahalo ea ka hammoho le tokafatso ea bohloko le bofokoli ka lipheletsong e ka tlaase nakong tsamaea. lipontšo joalo hangata e etsa hore ho ba le mamello ho ba thibela, hobane matšoao a le mong ea bitsoang hoo e ka bang ha itšoenye. Hangata ka ho fetisisa ho khesoa hona ha batho ba ba a pepesa ho ka lebaka la:
- sebelisa ho tlola ea joala le koae;
- nona haholo;
- ea mali e phahameng k'holeseterole;
- lefutso, 'me joalo-joalo.
Matšoao ka sehloohong
lefu Charcot e - ena ke boemo haholo a bohloko bo etsang hore ba boemong bo sa thabiseng ba le mamello 'me haholo sitisa boleng ba bophelo. Ka ho hana ena ea motho ea ba atisa ho tletleba ea mokhathala, hammoho e le boemong bo sa thabiseng le bohloko maoto ha a ntse a tsamaea, haholo-holo ka maraong le mesifa namane. Ho na le Maemong a moo bohloko localized ka lisele tse ka mesifa ea lirope le thekeng ho ea. E le bakuli ba nang le phumano ya lefu Charcot oa karolo e 'ngoe kokobela le fokola hang-hang ka mor'a hore motho a phomole tse khutšoanyane.
Ka lefu le joalo ka distal lipheletsong ka tlaase ea mokuli ba atisa ho hlokomela trophic le vegetative-vascular mafu a (mohlala, akrozianoz, maoto a batang, marbling tsa letlalo le liphetoho tse holofatsang, ho hloka pulse length ka methapo ea maoto le seso se kekang ea menoana ea, tseo hangata li fetela le proximally tataiso).
Ho phaella moo, lefu Lou Gehrig e tšoauoa ka liphetoho tse holofatsang le dystrophic ka masapo a ka le manonyeletso (hypertrophy dikarolo tsa motho ka mong, le degeneration tsa lefufuru, sequestrations lesapo, osteophyte, intraarticular le itlelang feela fractures la masapo a nako e telele). Ho phaella moo, laxity le fokotswa nahanela ba manonyeletso haholo ho eketsa kotsi ea likotsi sithabetsang.
lisosa tsa
Charcot e lefu - lefu le bakiloeng ke hlōloa ha methapo leoto (thromboangiitis, obliterans atherosclerosis, foromo pheriferale tsa aortoarteritis nonspecific joalo-joalo.). Bohloko le mamello etsahala ka lebaka la ho haella phallo ea mali ho mesifa dinama tse nyenyane tse ea lipheletsong tse tlaase. Hape, le maloetse ka 'na fella ka compression ea Kauda equina ka stenosis lesapo la mokokotlo, bonyane - ka lebaka la lesapo la mokokotlo khoele ischemia ka arteriovenous malformation, kapa atherosclerosis ea aorta ena.
kalafo ea lefu lena
Therapy hill claudication ke mohloli o ka sehloohong oa kalafo e tobileng ea lefu lena le, e leng methapo. Ka tloaelo ho, ka Maemong a joalo lingaka li ho eletsa bakuli ba tsona ba ho tela mekhoa e tsohle tse mpe, a lahleheloa ke boima ba 'mele le ho latela lijo tse thata-thata. Bakuli ba boetse ba fuoa kabelo ea sete khethehileng tsa boitlhakiso li mele, e neng e tla hlōla matšoao a lefu lena.
Ha e le mekhoa e sa khomaretse mekhoa e tloaetsoeng ea phekolo, joale ba akarelletsa ho fumana meriana e fapa-fapaneng. ketso ea bona e fana analgesic le vasodilator sebediswa. Hape famasi chelete thusa ho fokotsa k'holeseterole e maling le ho hlapholla lona.
Ba hlokang a hlobaetsang le ho kenella ho buoa sebelisoa ka tshebetso eo atolosa e mothapo lumen ke kenyelletsa ka e le catheter khethehileng.
Syndrome, Charcot-Marie-Tooth lefu
kheloha ena e emela sehlopha sa maloetse a se futsitseng, tse tsejoang ka degeneration tsa likhoele methapo ea kutlo pheriferale. Re lokela ho hlokomela hore variants fapaneng bitsoang lefu ka ho thehoa likoli fapaneng liphatsa tsa lefutso. Boholo ba mafu tsena li futsitseng ka autosomal laolang mochine. Leha ho le joalo, hona joale a tsebahatsa le embodiments tsa mafu a amanang le mamarello tsa X chromosome.
Ka tepelletse maikutlong a joalo, Charcot-Marie lefu, ka mamello ameha lesapong la mokokotlo 'me methapo pheriferale. Ho itšetlehile ka itseng liphatseng tsa lefutso sekoli batho ba ka etsoa axonal kapa demyelinating neuropathy.
Hangata ka ho fetisisa emeloang kheloha ka qala ho ntshetsa pele ka lilemo tsa bocha kapa lilemong tsa bocha. Matšoao a sehlopha sena lefu qetellong ba Amplified, 'me lefu le sa tsoela pele, eo ka eona le hlaha ka tsela e itseng ka toka ea bokooa, ha e isang lefung.
Matšoao a khesoa
lefu lena le qala ho hlaha ho tswa ho distal fokola mesifa le bofokoli ba lisele leoto. Ha nako e ntse, maoto a holofala le menoana e le khōlō le ho hammertoes. Ka bana ba nang le phumano ena e hoo e ka bang kamehla bone lieha ntshetsopeleng meleng.
Kalafo ea mafu a lefa
phekolo e itseng ea boemo joalo pathological ha e yo. Leha ho le joalo, ho ntlafatsa bophelo bo botle ba bakuli, lingaka boo hangata ho laela ea physiotherapy le phekolo mosebetsing. Ho phaella moo, bakuli ba tepelletse maikutlong ena ba ho pharaletseng sebelisoa mefuta eohle a maqheka tsa bongaka hore ho dumella ho felisa matšoao a bohloko. Ka mohlala, ha a leketlisitse maoto sebetsa masapo itokisa eketsa shank joalo joalo. Hape e na le boleng batlang e le khōlō ea tlhabollo liphatsa tsa lefutso.
lefu Von Willebrand e
Re lokela ho hlokomela hore e le hore mafu a lefa kenyeletsa se feela Charcot Syndrome. lefu Von Willebrand e ka boela ea a tšoaetsanoang ka ka ho beng haufi.
E le o tsejoa, kheloha e emeloang ke mafu a sa atileng ka ho fetisisa a lefa, ea isang ho ho qhala tsa coagulation mali kapa tsamaiso hoama. Leha ho le joalo, hangata e le lefu lena le hlaha ka tsela ea bophelo ka lebaka la maloetse a mang (ke hore, e fumanweng foromo).
matšoao a lefu
Kotsi ea tsoa mali ha kheloha joalo e fapane haholo ho itšetlehile ka mofuta o mong oa lefu. Likarolo ka sehloohong oa ho hloka taolo ena lefa ke mokola iphetang, gratuitous longoa le longoa, tsoa mali marenene, 'me joalo-joalo. Basali ba ka 'na ba e boima matsatsing nako,' me ha a hlaha kotsi ea ho lahleheloa ke e ngata ea mali.
kalafo ea lefu lena
Bakuli ba tepelletse maikutlong ena ha kalafo e hlokahalang, empa menyetla ea ho tsoa mali ka tsela e feteletseng ba kamehla kgothaletswa. Kahoo, ba le mamello ho ka buelloa hore a lithethefatsi tse fokotsa letšoao hlakileng ea lefu lena. Ha mokuli e lokiselitsoe ho etsa ho buuoa, ngaka e lokela ho phetha kalafo e thibelang.
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